ZempiloDiseases and nemibandela

Myasthenia gravis: ntoni na? Oonobangela, Iimpawu kunye Iindlela Treatment

Myasthenia ngokuba sisifo leyo sikhatshwa ngokwanda buthathaka kwezihlunu. Isifo efanayo echazwe kuqala ngo-1672. Ngokutsho manani, esi sifo lungenzeki rhoqo kakhulu. Noko ke, abantu abaninzi abanomdla imibuzo ngokuba kutheni kukho into eyindoda, yintoni na yaye oko yayingako imiqondiso bamlandela. Ngapha koko, isigulo kwangethuba kuxhomekeke rejimeni kwaye umgangatho wobomi umntu ogulayo.

Myasthenia gravis - ntoni na? Izinto ezibangela izifo

Ukuba yonke into eqhelekileyo, acetylcholine phezu excitation Asikokungena zicandwe zobuchopho, aye receptors ezithile inwebu imisipha - ngoko iyavuseleleka nokucuthwa imicu kwezihlunu. Kodwa kwiintsana, le indlela yokosulela kwe umlawuli angxamele-luvo yaphulwe.

Ngoko nangoko ke kubalulekile ukuphawula ukuba myasthenia gravis - isifo yemfuza. Kwaye namhlanje isigqibo sokwabela iintlobo ezimbini ezisisiseko yophuhliso lwayo. Kwezinye iimeko, ukwahluleka ukudluliselwa luvo ngokwentshukumisa unxulunyaniswa uphazamiseko kwindlela eqhelekileyo yokusebenza le ngxenye. Enye imbangela oqhelekileyo esi sifo i sisilonda esidumbileyoesingaphakathi samathambo le nobubovu thymus, nto leyo ekhokelela ekuhleni mali kuhlelwe acetylcholine.

Kukho myasthenia ebizwa njalo-lweentsana gravis. Yintoni na? Olu hlobo esi sifo kwenzeka xa kuzalwa ukuba oomama babo baphathwa ukuphazamiseka of Uhanjiso neuromuscular.

Iimpawu zesi sifo ngazo njengakwimihla zokuqala emva kokuzalwa, yaye abantu abadala kuphela. Kukho izinto ezithile ingozi leyo enokwenza ukuba myasthenia asakhasayo gravis. Izizathu uhlaselo buthathaka kwezihlunu kunokuba ngenxa luxinzelelo olungamandla, ntshikilelo luvo, izifo ezosulelayo elidlulileyo kunye ukuphazamiseka kwamajoni omzimba.

Eyona engundoqo zesifo myasthenia gravis

Njengoko sele kukhankanyiwe, iphambili esi sifo buthathaka kwezihlunu. Ngentsasa elandelayo, izigulane badla bazive eqhelekileyo. Kodwa kweeyure ezimbalwa kamva izihlunu skeletal angakhathali ayeke ukusebenza, ukugqiba ukukhubazeka. Emva kokuphumla ubuchule ukunciphisa wachacha.

Ngokuxhomekeke kwiqela abachaphazelekayo imizwa wahlulwe iintlobo ezintathu ezingundoqo sifo:

  • Lidla esi sifo ichaphazela izihlunu, apho innervated yi luvo cranial. Kwaye ke iphambili kule meko ptosis. Ukuba umntu ukuphumla ngokupheleleyo vula amehlo akho, ngoko emva kweeyure ezimbalwa, kukho zibhetyebhetye chu zokusa eliphezulu.
  • Kukho kwakhona bulbar myasthenia gravis. Yintoni na? Esi sifo ihamba ukophulwa ugqithiso luvo angxamele kwizihlunu, leyo onoxanduva igwinya, ukuhlafuna kunye nezinye iinkqubo. Izigulana zabantu abanengxaki yokutya, kwakunye utshintsho ngokuthe ngcembe ilizwi, de Ukunyamalala kwayo ngokupheleleyo.
  • Xa uhlobo kakhulu jikelele le isifo eso, apho izihlunu iliso ayachaphazeleka kuqala, ngoko ke inkqubo uyemka entanyeni, eziphelweni aphezulu, njalo-njalo. D.

Iindlela zonyango lwe myasthenia

Kubalulekile ukuphawula ukuba myasthenia sifo gravis kuyingozi kakhulu kwaye kufuna inkathalo abanezakhono. Inyaniso kukuba esi sifo sizibonakalisa yi ngeentlekele ebizwa ngokuba yiyo, apho sikhatshwe ukushwabana izihlunu yokuphefumla okwethutyana, kwaye oku kubeka engozini ubomi.

Unyango olusebenzayo kuphela obuyiyo neziyobisi acetylcholinesterase - i "Proserpine" yaye "Kalimin". Ezo therapy lokugqibela iminyaka, kwaye umthamo wamayeza esoloko itshintsha ngokuxhomekeke kurhulumente kunye nezinga nophuhliso sifo. Ukuba myasthenia gravis kujongwe kwimvelaphi ithumba le nobubovu thymus, utyando yenzelwa ukususa umzimba.

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