Isifo myopathy - ntoni na?

Abaninzi baye beva ngale isifo myopathy. Yintoni na loo nto, uyazi ukuba wonke umntu. Igama elithi "myopathy" idibanisa eziliqela nezifo kuphazanyiswa apho contractile Ukubanako imicu izihlunu kwaye kuphuhlisa buthathaka kwezihlunu. Ngenxa yoko, ukuhla umthamo iintshukumo esebenzayo, imvakalozwi ukuhla, yoma, kwaye kwezinye izihlunu iimeko psevdogipertrofiya. Kwakhona phantsi myopathy ukuqonda yonke ngezifo kwezihlunu skeletal. Isifo kakhulu kangangokuba indalo ilifa, kodwa kwakhona ukuphuhlisa ngenxa yokwenzakala okanye izifo. Okunye bangenwe myopathy yeha.

Myopathy - yintoni na kwaye zeziphi na iintlobo ezahlukeneyo zesi sifo?

A iintlobo ezohlukileyo sifo kakhulu. myopathy zilandelayo common kakhulu:

• ukuba uneDuchenne;

• Landuzi-Dejerine;

• Becker;

• Erb and Erb-Rot;

• Amyotrophy Werding-Hoffmann;

• Amyotrophy Kugelberg-Welander et al.

Le fom kakhulu kakhulu kwaye uninzi yaziwa kakuhle esi sifo myopathy uneDuchenne kaThixo. Lubonakala yi kukho isiphene ilifa le dystrophin - iproteni egcina ingqibelelo imicu kwezihlunu. Kule fomu kwesi sifo kukho ukunqongophala ngokupheleleyo oko.

Myopathy: iimpawu

Uphawu iphambili sifo kakhulu buthathaka kwezihlunu. Ngamanye amaxesha kuba ukutshintshwa kwimicu zeethishu izihlunu adipose, nto leyo ekhokelela hypertrophy zabo. Baba eqinileyo kwaye kunzima ukuya ngaphandle kwebala kunye elastic. Izigulana myopathy iqinelwa waddle isici. Ngokuqhelekileyo, ubuthathaka yaseBougainville kwiminyaka 8-10. Abantwana kuba nzima ukuhamba, yaye le ikhono zazilahlekile ukuya kwiminyaka eli-12. Ngeli xesha baqale zokufota, contractures ngokudibeneyo, oko luyenyuka ngokunciphisa umsebenzi. Ezinye izigulane unesifo iqola ingqondo yalityaziswa kunako ukubonwa kwi zigaba ezilandelayo ukusilela kwentliziyo. Abantu abaphila nale unesifo-avareji engama-20. Eyona nobangela wokufa ezesifuba ukusilela zokuphefumla.

Myopathy: unyango lwesifo

Uthomalaliso kwesifo ikakhulu ijolise ekwakheni microcirculation kunye yokucolwa in izihlunu kunye neenkqubo luvo. Ukulungiselela le njongo, ukusetyenziswa arhente steroid, iivithamini, iziyobisi potassium, mziba biogenic, iziyobisi amanyathelo trophotropic, arhente anticholinesterase, iziyobisi vasoactive.

Kwakhona, ukuba myopathy iluncedo kakhulu yokuthanjiswa konwaywa umzimba uphela. Ngenxa yale nkqubo, ukujikeleza kwegazi iyavuseleleka, ukuphelisa stasis igazi, ukwanda igazi kwemali kwizihlunu. Ukongeza, isiphumo esihle umsebenzi kuyenzeka, bezihlikihla, hot ibhafu kunye netyuwa elwandle.

Ngenxa yoko, siye sahlolisisa ingqiqo ka "myopathy", yintoni na kwaye yintoni na imigaqo yonyango kwesi sifo. Kodwa, nkqu onjalo unesifo kufuna ukuthotyelwa kunye izidlo ezithile. Oku kubandakanya exclusion iziselo ezinxilisayo, nenqatha umda, okuneziqholo, ukutya ezinetyuwa, kunye neemveliso inyama. inani okunikezelwe ubisi hi mpimo mda, salads celery, iisiriyeli amanzi okuziinkozo ziyantshuliswa ingqolowa, ama-apile, isibindi, ioli kajongilanga kunye lesi ulwandle.

Ngoku, ukuba nithe nafika kulo igama elithi "myopathy", yintoni na, emva kokufunda inqaku sele uyazi.