Yintoni eyenza Brugada syndrome?

Ngokutsho kweengcali, Brugada syndrome ibekwe kwi kudidi nesifo sentliziyo lokuqala zombane kunye nengozi enkulu kakhulu-ebizwa ngokuba 'aritimicheskoy ukufa ngequbuliso ". Esi sifo ngokuqhelekileyo sikhatshwe rhoqo eliphezulu ventricular fibrillation, kunye ST ingxenye ephakamileyo.

lwezifo

Kukholelwa ukuba Brugada syndrome sinesifo rhoqo ka-4 ukuya kuma-12% yazo zonke iimeko ezikhoyo ukufa ngesiquphe ngenxa yeentlobo ezahlukeneyo izifo zentliziyo. Ngokutsho kweengcali, esi sifo ethile livela izihlandlo ezili-10 rhoqo kwisiqingatha iinkunzi yabemi.

izizathu ezibonakala

Okwangoku, izinto zokugqibela esi sifo ayiqondwa ngokupheleleyo. Noko ke, oogqirha bakholelwa ukuba xa zofuzo -ebizwa ngokuba 'sodium channel "amathuba SCN5A sophuhliso oluthe kwesi sifo.

Brugada syndrome: Iimpawu ECG

Okokuqala kufanele kuqatshelwe ukuba iimpawu zaseprayimari ngokuqhelekileyo ukwasuleleka ngabantu emva kweminyaka engamashumi amane. Ngoko ke, oogqirha zezona zinto zilandelayo kubonisa ubukho besi sifo:

• ezikwenza ukuphazamiseka nokuphefumla ikakhulu ebusuku;
• syncope;
• tachycardia ventricular polymorphic;
• iziqephu ventricular fibrillation.

unyango

Xa isigulo ezifana Brugada syndrome, ikakhulu ECG ibonisa ukuphambuka kunokwenzeka ukususela impilo eqhelekileyo isigulane. Njengoko unyango lokuqala iingcali rhoqo ukumisela ichiza "quinidine" kunye nezinye iindlela, kuquka "Isoproterenol" iziyobisi. Ngokuphathelele yokugqibela, loo nto ithathwa iyeza esebenzayo kakhulu ukuba uyakwazi Ekutyunyuzweni ngokoqobo i "uqhwithela sombane" elivela kwizigulane kunye nokugula ebusuku. Njengoko le ndlela iphambili zokuthintela ebizwa ngokuba "ukufa ngequbuliso" yomguli, oogqirha Sicebisa ukufaka esisa-mshini. Kufuneka kuqatshelwe ukuba xa kwafunyaniswa Brugada syndrome, kungekho ukwenza izinto lwangaphandle sifo kufuneka kube rhoqo babonwe ziingcali. Nangona kunjalo, akukho kufuneka oluchazwe apha ngentla umzila esisa-defibrillator kule meko.

amanyathelo othintelo

Okwangoku, Brugada syndrome banesifo kakhulu kunqabile. Njengoko amanyathelo othintelo , oogqirha bayacetyiswa ngamandla ukuba behlolwa rhoqo. Oku kuthetha ukwenza yonke uxilongo ezinkulu, kubandakanywa i electrocardiogram, iimvavanyo zegazi iimvavanyo nomchamo. Eyona nto kukuba kule macandelo kwaye bagwebe ubukho iingxaki emzimbeni. Qaphela ukuba ubukho "izalamane 'ekupheleni uxilongo kunyanzelekile ukuba enze uviwo enenkcukacha, mvisiswano leyo, kwelinye icala, kuthetha ukuba ingcaciso le ebizwa ngokuba" umngcipheko base "kwakunye esweni kwe-nomonde kangangexesha elide, kuxhomekeke zezempilo ngamnye . Kuphela ngale ndlela, njengoko kubonisa, unako ukukuphepha ukufa, iingxaki kunokwenzeka emva, kunye nokuthintela izifo nkqu nisaqala kakhulu kuphuhliso. Hlala uphilile!