Zempilo, Amayeza
Vasculitis - isifo kwaye afumane unyango
Vasculitis - isifo ezinxulumene neenkqubo ukudumba kwindawo emithanjeni. Le komtshiso oko kwenzeka ngenxa yezizathu ezahlukeneyo. Kodwa kaninzi vasculitis - utshitshiseke ezenziwa iintsholongwane okanye neentsholongwane ezibangela amajoni omzimba ukulwa inyama yento ephilayo yayo efanayo, kuquka - ngokuchasene izihlunu nemithambo. Ngoko ke vasculitis libhekisela kwiqela kwezifo sokuhlasela. kubangelwa - ayikho kuphela ifuthe zosulelo. Ngokubanzi, unyango kudla vasculitis nzima kukuba inzululwazi akazi yonke enye into malunga nesifo, kuquka izinto zayo, indima ufuzo njalo-njalo. Kukho ukuhlelwa esi sifo, leyo yahlula oko eziziprayimari nezizisekondari.
vasculitis Primary kunokwenzeka ngenxa yofuzo kuyo, izifo, iintlobo zokwenzakala kunye namayeza athile. vasculitis Secondary kaninzi kwenzeka ngenxa naziphi na iingxaki esi sifo. izifo basenokuba ngumkhuhlane nebomvu, umhlaza, ukhwekhwe, kunye meningitis.
Kukho amaqela ezininzi vasculitis na. Iqela lokuqala - sisifo esichaphazela imikhumbi emikhulu. Casa iseli giant arteritis, apho kukho igazi, ifiva, iimpawu ezithile rheumatism. arteritis Takayasu kaThixo, echaphazela kakubi aorta ibangela ischemia.
Iqela lesibini izitya vasculitis kuchaphazela ixabiso avareji. Eli qela libandakanya samathambo knotty - oko kuchaphazela imithambo ezinkulu amalungu - intliziyo, izintso, imiphunga, isibindi. Vasculitis ebantwaneni kaninzi kwenzeka ngohlobo Kasavaki syndrome, nto leyo ichazwe kwi izitshanguba ze ancedisana kwiinwebu emlonyeni - umzekelo, uqala ukwambula kumphezulu ulwimi, amehlo akhe redden. Izandla neenyawo kuvela ukudumba, kuphuma ubushushu kunye nokunyuka kwiindawo entanyeni nkovu.
Iqela lesithathu iquka ukoyisa izitya ezincinane. Oku kunokuba, umzekelo, granulomatosis Wegener kaThixo, nto leyo isasazwa kwi yomoya eliphezulu kwaye wabonakaliswa ngokohlobo ngeempumlo - ubomvu zixutywe ngokupheleleyo inegazi.
ingqalelo Ngokuqhelekileyo ngaphezulu ngokuhlawula ezo vasculitis, apho zimelwe komtshiso kwemithambo yegazi. Eli qela vasculitis lwahlulwe ngeentlobo komzimba kunye non-komzimba. Andidibani ngokuqhelekileyo ezinxulumene kolusu kunye kwizihlunu visceral. ukudumba Non-komzimba kakhulu limelwe isikhumba isigulane.
Vasculitis esikhumba - esi sifo kuqhelekile ngaphezu kokuba vasculitis systemic. Nale nkqubo unyango - inkqubo kuba kunzima kakhulu futhi. Isizathu ilula - sisifo zenkqubo luphawulwa yinto yokuba akukho namnye kodwa eziliqela amaziko lonke isigulo ubani enokuthabatha inxaxheba. vasculitis Systemic ukuvelisa iimpawu ezifana hemorrhages ezincinane kakhulu eluswini, ifiva, kunye nelahleko ezinye izibilini. Njengoko uhlobo vasculitis systemic ukwahlula ukopha vasculitis - kolusu ezininzi kunye kwiinwebu umzimba. Kodwa ke arhabaxa esikule namalungu amanye amalungu zangaphakathi.
Kubonakala amaninzi ukopha vasculitis ebantwaneni, nto leyo neminyaka eli-14 ubudala. Esi sifo i esosulelayo-komzimba. Sophele vasculitis kubantwana sibi, ichaphazela kwingoma ulusu microcircular, izintso, amalunga, eli phecana zesisu kunye namanye amaziko. Iimpawu: mhlawumbi indibanisela esiswini, ukopha, edibeneyo, nomkhuhlane. Irhashalala, nto leyo ebonakalisa nesi sifo, bemelwe yi hemorrhages ezincinane symmetrically ukubonakala iingalo ukugoba, imilenze. ixesha elithile emva kokuzalwa kwalo kokuba baqale ezimfusa, ngoko - kuba luthuthu. Iziseko Ezinye umbala iba brawuni lube yellow. Vasculitis ebantwaneni kaninzi kubonwa kunye nezinye izifo, kuquka yidityaniso, tonsils ezingapheliyo kunye nosuleleko TB. Usulelo okanye esinye isizathu kuphucula ubuntununtunu yomzimba. Against le zegazi kubonakala yokusabela hyperergic. Kwaye kungakhokelela ekubeni kubekho inguqu kwinkqubo ye coagulation igazi kunye ezisebenza yintshukumo yamajoni omzimba.
Xa lokufunyaniswa unyango vasculitis kubandakanya ahlale yesigulane kwi bedrest de amanxeba shwaka, bakhutshelwa ngaphandle kwizidlo zonke zamavumba kunokwenzeka ukuba okunokuqulathwa ku iziqhamo citrus, itshokolethi kunye ikoko, amaqanda, njalo njalo. Ukongeza, unyango kusetyenziswa antiplatelets, anticoagulants, desensitizing, hormone kunye nezinye iziyobisi. Unyango lwe vasculitis ebantwaneni ezingakhona imo polupostelnom emva kweentsuku ezimbalwa emva yokuduka yabangxamayo. Ukunyhashwa contraindicated ngokungqongqo. Ukuba kukho iindima izifo ezingapheliyo, xa unyango unyango vasculitis zintsholongwane ayiqukwanga (okt. A. Kukho umngcipheko ziyabagulisa). Ukuba isifo kunzima, kuyimfuneko ukusebenzisa iziyobisi immunosuppressive.
Ngoku, ngelishwa, phi kaninzi ngaphezu ngaphambili, wafumana unesifo vasculitis. Ukunyanga ke, kuqala kwiinto zonke, ukuba ukunciphisa indlela abazazi iimpawu abasekho akhule kwaye aphuhle. Kuyimfuneko ukuba okukwazi nxamnye kwinyama omzimba baye bayeka. amachiza Suppressive (immunosuppressants) uncedo ukuba "umoya" imikhosi yamajoni omzimba eyenzelwe ukuhlasela kwinyama komzimba, babuvayo kweli nqanaba uqalisa umva a vasculitis kancinane. Ukuphatha kuyo kwinyathelo lesibini ijolise ukubuyisela umzimba umonakalo.
Uxilongo lwe vasculitis iquka ucalulo lwemizekelo umchamo kunye negazi, isifundo likarhulumente iimpahla, X-reyi kunye biopsy. Ngaphezu naziphi na ezinye iintlobo, yingozi vasculitis lwenkqubo. Unyango busekelwe phezu nolawulo immunoglobulins asebenzisa iziyobisi cytotoxic, ohlambululayo igazi, ukuthatha amayeza ezinciphisa ukukwazi igazi ukuba ihlwili.
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