ZempiloDiseases and nemibandela

Myasthenia gravis: iimpawu, izinto, unyango

Igama elithi "gravis" sele ngokoqobo eliguqulelwa ngokuthi "buthathaka kwezihlunu". Ngaphezu sifo Isihloko okuninzi nezinye: ukukhubazeka bulbar, ophthalmoplegia asthenic, isifo Goldflam, zophendlo lwezifo eqatha fatigue syndrome. Kuyinto sisifo samathambo. Oku kuthetha ukuba abantu kukho omzimba ukutshabalalisa iiseli eziyingozi kwaye iintsholongwane, bambulale iiseli eziqhelekileyo esempilweni.

Myasthenia gravis, nto leyo efana iimpawu zesifo milestones amatyala, rhoqo ukukhulisa ekuhlanganisweni kweentombi ngaphantsi kweminyaka iminyaka emashumi mane. Bonke abantu 10 ngaphandle ezilikhulu lamawaka namhlanje abafunyaniswe myasthenia gravis. Iimpawu zesi sifo:

• Umbono kabini ngokuhlwa, iliso ukudinwa, ukuthotywa ubudala;

• ngokuhlwa hoarseness, kwemisipha nokudinwa emva elide ukulayisha ilizwi;

• kakhulu fatigue ;

• Ukophulwa izakhono motor ocoliweyo;

• ukuncipha uvakalelo;

• ukuphazamiseka intshukumo, ingakumbi ngexesha iintshukumo phinda;

• ukuphazamiseka yokuginya, ukutya ukuba angene impumlo, ilizwi ngeempumlo;

• ziba ku ukuphefumla.

Abaninzi abagulayo kuqatshelwe ukuba i-fatigue ubushushu kwandisa kakhulu, kwaye kwakhona kwenzeka ngokukhawuleza kangangoko ukudinwa.

Le myasthenia obungena gravis? Iimpawu zaso ungaya kuyabonwa iminyaka emininzi. Ngu uhlobo esi sifo kuba izinzile okanye, kwiimeko ezininzi, progressive. ifomu umile ibonakala kuphela xa unyango nokungaphumeleli kwawo.

Progressive uyakwazi ukuphuhlisa kwisithuba seenyanga ezintandathu (nkqi), kwiiveki ezintandathu (rough), iiveki ezimbini (amabi). Myasthenia gravis, ogama iimpawu kuqala wayibona, kuquka zonke iinkalo ezidweliswe ngasentla. Xa unyango ngaphambi ebulalayo myalgia, mpawu ezo ikhula ngokukhawuleza kakhulu, kunokukhokelela nokungakwazi.

Imilo lika-myasthenia gravis yahlulwe zobulali (rhoqo iliso) kunye nefomu ngokubanzi. Myasthenia gravis, uhlobo ngokubanzi ochaphazela iqela amalungu ezininzi, kwafunyaniswa ukuba iikliniki luvo. Moshilongo kuyimfuneko ukubamba ikhompyutha kunye livakale magnetic Itomography, pnevmomediastinografiyu, prozerinovye isampula. Faka kwakhona biopsy yethishyu dystrophy, izifundo somatic jikelele, ngokuhlahlela yemfuza, electroneurogram.

Ukuba une myasthenia gravis, unyango ixhomekeke yimiqolo ezinkulu ezintathu:

• Amanqanaba.

• Ukudibana iintlobo ezahlukeneyo (ukubuyekeza, non-ngqo, pathogenetic) unyango.

• Ukususwa kwisigaba ahlekise.

Ngethuba lesigaba imbuyekezo, unyango esuke iziyobisi anticholinesterase veroshpiron, methylsulfate neostigmine, potassium chloride. Kule yesibini inqanaba, kwiimeko kakhulu ukuze kuboniswe thymectomy - kususwa thymus. Ngowe-75% amatyala, lo msebenzi kukhokelela ukugqiba alulame, kwabanye - ekuphuculweni ebonakalayo. Lo msebenzi kwenziwa eqhelekileyo indlela ezonakalisayo kunye encinane esibuhlungu.

Emva kotyando (ngamanye amaxesha kunokuba) ukumisela iziyobisi glucocorticoid. unyango olunjalo ekukhethwa ukuba lwenziwe esibhedlele, phantsi kweliso labezempilo. Isigaba sesithathu yonyango myasthenia gravis - immunosuppressants ukuqeshwa.

iindlela sesiko azisinyangi isifo akwenzeki, kodwa kuhamba unyango ephambili ukuba oogqirha musa engqondweni. Umzekelo, iglasi na iyabiliswa oat lathi mayiyo kundithengela amanzi, bilisa iikota ezintathu yeyure, iyure enye uze uwutshise waxhuzula ubusi, yokuyifaka kulwelo isiqingatha indebe kane ngemini. Enye iresiphi kunzima ngakumbi ukuze ulungiselele. Bathathu wacanda iintloko blender begalikhi, ugalelwe ioli ezazidityaniswa lemons ezine, fakela Kilo ubusi kunye iglasi yeoli linseed. Lo mxube kuthathwa kathathu ngemini.

Sele ekunyango lwe myasthenia gravis, kufuneka ukhumbule ukuba oko kuya kunceda kuphela ukuba indlela yokuphila esempilweni.

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