ZempiloDiseases and nemibandela

Kutheni tho ezinzwaneni? iinzwane tho kuzalwa: Oonobangela

Fine, ukuba umntwana ezelwe uphilile! Kodwa maxa wambi abazali bayothuka ukuba uyifumana iyinto engaqhelekanga kunye iziphene. Ngokomzekelo, iinzwane ezinyibilikiswe olusana. Izinto ezibangela le sifo maxa wambi zibe bachaza ukuba intsapho yazo kuthiwa uphawu olulodwa idluliselwa ukusuka kwisizukulwana ukuya kwisizukulwana, kodwa maxa wambi ukuze baqonde oko kwadala nophuhliso isiphene yandiswa ngumba, kunzima kakhulu. Loo nto syndactyly (ngxubevange iminwe eliphezulu okanye iziphelo aphantsi), yaye kutheni yenzeka, yaye siza kuthetha ngayo kwinqaku lethu.

Syndactyly akuxhaphakanga

Ifumaneka umntwana edidekile iinzwane kunye nezandla ayinakutshintshwa ezinqabileyo kakhulu - xa omnye, lo kuzalwa 2-3 amawaka. Ke amantombazana ufumaneka amaxesha-2 ngaphantsi ivame kakhulu amakhwenkwe. Ihlanganiswa lingama-2 no-3 iinzwane okanye iminwe ophakathi umsesane esandleni. Amaninzi, oku fusion akuthethi buhlungu kwamalungu imisipha, eyenza kuphela ingxaki izithambiso.

Kwaye ukuba iminwe idla phantsi yokuzahlula ngotyando, iinyawo badla ningachukumisi ngaphandle kokubona unesiphene imiqobo ingakumbi kuphuhliso womntwana (kukophula onjalo abadli kuphazamisana ngokuhamba oqhelekileyo). Nangona kunjalo, phambi syndactyly ngo-60% yezi bantwana rhoqo afumaneka kwezinye ukungaqheleki iziphene omzimba - ngonyawo nesilima, pseudarthrosis, kokukhubazeka, etc ...

iinzwane tho kuzalwa: Ubangela Pathology

Yintoni ekwenyukeni ukubonakala syndactyly? Inyaniso kukuba lo iminwe neenzwane usana ilele phezu weveki 4-5 zokukhulelwa, xa unina lidla akukho nto malunga noko, kodwa ngenxa yokuba akukho nto ayithi simele ngokwakhe. Ukusuka apha kukho amathuba eliphezulu ukuba Ingane kuchaphazela iingozi - ..-X-reyi, imithi, utywala, icuba, njl Asinako ngaphandle ubungozi nemiphumela emibi ngenxa umfazi omithiyo umntwana wakhe kwizifo ezifana influenza, mumps okanye negcushuwa.

Kwaye ke zizathu zixhaphakileyo ukuba usana edidekile iinzwane libhekisela lufuzo nje ocande kubazali abantwana.

Ngokuzenzekelayo, xa sibona i syndactyly umntwana nokuba inobulali, kufuneka ihlolwe ukuba ubukho yemfuza chromosomal syndromes (syndrome Apert, Poland okanye Edwards), apho ezo iminwe yi iliphawu na iziphene ezinkulu wosana.

Hi ndlela leyi, ku yezonyango zabona amatyala ezifunyenwe azikhuli iminwe ngenxa kwemichiza okanye thermal ibhrashi wokukhusela okanye ngonyawo.

Ukuba mabenze ntoni xa usana edidekile iinzwane kunye nezandla, kuya kuxoxwa kamva, kodwa ngoku nentwana theory.

Pathology ezithathwa

Xa amayeza, ngonobangela wokufa baphathwa sithi zihlelwa kuxhomekeke imeko amathambo kunye neqondo coalescence. Ngoko ke, yi ngokohlobo azikhuli zeethishu eliphantsi syndactyly nethambo, kwaye fusion inkulu - epheleleyo kwaye zingagqibeki.

Kuxhomekeka ngeenzwane ukuba ihlanganiswa ngayo okanye syndactyly esandleni ngu:

  • isikhumba membranous - phakathi kweminwe babe inwebu yesikhumba (olu hlobo ngezifo yeyona lula);
  • isikhumba - phakathi kweminwe kufuneka ulusu ubukhulu ukuya ancedisana engundoqo ethambileyo, abaninzi ngokuqhelekileyo yonke ubude neminwe;
  • ithambo - fusion kwenzeka kwinqanaba le phalanges, kwaye bakholisa ngokwaneleyo okanye zikhubazekile;
  • ukudibanisa - kukho iintlobo ezininzi syndactyly (le fomu kucingwa kakhulu nzima ukunyanga).

isifo syndactyly

Ngokuqhelekileyo, bonisa syndactyly kwiiyure yokuqala yobomi usana, xa usibona neonatologist yayo. Xa usana sele ihlanganiswa iinzwane, ngoko ke umbuzo imfuneko kutyando ngokuqhelekileyo angafanele kuyo ngamandla, kwaye abazali kufuneka ithuba bahlaziye iingenelo bendlela zotyando.

Ukuze ube nomfanekiso ngokupheleleyo ngezifo, usana kufuneka sibonise ugqirha wabantwana uze wenze-X-reyi ye ngeenyawo uqikelelo ezimbini. Oku kuya kuqinisekisa iimpawu unesiphako kunye nemeko amathambo kunye namalungu wosana.

Njani syndactyly

Ukanti, akukho nokuba kutheni iinzwane tho, unyango kuphela kwesi sifo uqhaqho.

Iminyaka yobudala kangangoko kule itakane - iminyaka 4-5. Noko ke, kulo mzekelo, ukuba iqhagamshele yesiphelo phalanges, umsebenzi kungcono kwenziwa phambi kokuba bebudala bungaphantsi konyaka omnye, ukwenzela ukuthintela ukukhula engalinganiyo leminwe deformation zabo.

imisebenzi syndactyly zolungiso bohlulwa babe ngamaqela 5:

  1. kunqunyulwa lula ingenamthungo membranous.
  2. Asike ne plasty imvaba kwizihlunu zasekuhlaleni.
  3. Asike yesikhumba kunye zeplastiki usebenzisa polnosloynogo okanye sihlume isikhumba uphuphu.
  4. Asike yesikhumba usebenzisa iiplastiki zidibene (usebenzisa autotransplantanty simahla okanye kwizihlunu zasekuhlaleni).
  5. Operation kwizigaba eziliqela, kuquka ithambo, imicu, izihlunu, nesikhumba yokumilisela.

Yiyiphi imisebenzi elandelayo iza kuba yeyona ilungileyo, ugqirha uza isigqibo, xa kuthathelwa ingqalelo uhlobo neentlobo ngezifo.

Ithuba postoperative: njengoko toe ezinyibilikiswe?

Emva kwethuba utyando recovery ludla ngokwenziwa ekhaya. Yalityatya ngeli xesha kufuneka lokuphumla (ngenyanga). Kuyimfuneko ukuba bayithobele yonke imiyalelo kagqirha, ukuqinisekisa inkathalo efanelekileyo amanxeba post-operative.

Ukuba ukunciphisa nangokurhala, ukuphelisa amanxeba, nentambiso yamehlo "Dermazin" okanye gel "Kontraktubeks", yaye emva kweminyaka esi-7 kweeveki, ngokutsho kagqirha, qala ukuya ukuyifundisa. Hi ndlela leyi, zinike ixesha kunye oku ukwenza oko - ukuvumela amanxeba zotyando okuphilisa kakuhle, ukwenzela ukuba zenze iintlungu umntwana ngexesha iinkqubo ezintsha.

Kwezinye iimeko, nabo bamele baqashwe kwaye ukunxitywa braces turbokasta ebisebenza phezu iminwe ezinyibilikiswe amalungu. Ekuqaleni (kwinyanga) kuzigqiba rhoqo kubo, uze uyibeke phezu kuphela ngexesha ubuthongo.

Kufuneka kuqatshelwe ukuba kuthotyelwe zonke iimfuno uya kukhawuleza akulibale ngale ngxaki siya sisa (iinzwane umntwana ezinyibilikiswe). Isigulane ndibuhluthe ngokukhawuleza kwaye ngaphandle iingxaki.

Outlook

Nangona isibakala sokuba namatyala syndactyly ngexesha lethu landa, ngoko ukuba abaphandi musa ukufumana ingcaciso eyaneleyo, ALS kwesi sifo kakhulu intle. iindlela zale mihla kunyango ukuze buncothulwe unesiphako, abuyisele yonke imisebenzi isandla okanye unyawo nokulungisa sengozini neminwe.

Xa usana sele ihlanganiswa iminwe umlenze okanye ingalo, umsebenzi yenza kube lula ukwenza iindawo eziqhelekileyo interdigital lo gama kugcinwe ukushukumiseka ngokuhlangeneyo kunye novakalelo weminwe yesigulana. Oko kukuthi, ukuba yasusa naziphi na iingxaki ezihambisana syndactyly.

Ingaba kufuneka wenze utyando ezinzwaneni syndactyly

Phantse njalo, abazali kufuneka ukufumana iingxaki zakhe usana kunye eminweni yakhe baqalisa ukuba inyanzelise utyando ngoko nangoko. Kodwa ukuba tho iminwe ngokwenene uhlangulayo akunjalo, kodwa iingxaki kuphela yobuhle emzimbeni, kwimeko apho kukho isiphako kule milenze, ingakumbi xa iminwe yakho nje gqitha yaye ukugoba eziqhelekileyo, ungenza ngaphandle uqhaqho.

Ukuba ibhinqa liye ihlanganiswa iinzwane ingadala neemvakalelo ezingakhiyo de nokungafuni ukunxiba izihlangu okanye bengenambadada ehamba elunxwemeni, ukuba lisekhona na akuyi kuba umntwana, njengokuba umthetho, ingxaki enjalo, Kakade, kunye sengqondo ekunene ukuya kuyo. Abantu abaninzi bahlala ngaphandle abazifumana kabi evela iminwe edidekile ezinyaweni zakhe. Kwaye abanye oko kunto uphawu ekhethekileyo twist yokuqala. Njengoko ubona, konke oko kuxhomekeke uyamamkela wena njengoko nawe na.

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