Isifo Rasmussen kaThixo (kobuchopho). Izizathu Rasmussen syndrome

isifo Rasmussen lelakhe kudidi kwezifo enqabileyo ukudumba qwele ebuchotsheni. Le kobuchopho ngokuqhelekileyo kwenzeka abantwana abangaphantsi kweminyaka eli-15. Amaninzi, isigulo eso sifo e ubudala. Xa abafikisayo kunye nabantu abadala, olu hlobo kobuchopho kunqabile kakhulu.

Le nkqubo ibandakanya enye okanye ezinye ikhweyitha obuchopho. Njengokuba isifo siqhubeka, oogqirha waphawula ukuba yome progressive. Oogqirha bathi ukuba uxhathiso ngokugqithiseleyo zonyango sifo. Enyanisweni, isifo Rasmussen - kobuchopho kunye neempawu ezithile asinyangeki.

ezibangela bha kobuchopho Rasmussen

Kude kube umyalezo we esi sifo iye ayasekwa. Izazinzulu ezichongiweyo kuphela zinto zintathu ezingundoqo ukuba ungakwazi ukuqala nokonga nokuqhubela phambili imeko zophendlo lwezifo evela kwinkqubo luvo. A nobuninzi kumagqirha bakholelwa ukuba Rasmussen syndrome kubangelwa omzimba samathambo, iintsholongwane kunye cytotoxic T-lymphocyte.

Indima enokubakho cytomegalovirus, leyo uyazimela neuron zezigulane abadala. Kungenzeka ukuba ezi kwamagciwane kubangela nangokurhala, zibe yokugula esinganyangekiyo. Ukongezelela, oko sivete ezinobuzaza wabonakala emva usuleleko kwangaphambili.

Ngoku, izazinzulu zikholelwa ukuba i mbewu yesifo samathambo unobangela kobuchopho Rasmussen. Izinto ezibangela isifo nalo kukholelwa ukuba kuchazwe yi cytotoxic T-lymphocyte.

Xa izigulane Rasmussen engqondweni, maxa wambi naphakathi kwezalamane abaphethwe nezinye izifo sokuhlasela. Umzekelo, isifo Behçet kaThixo. Oku kubonisa hypothesis izalamane inxaxheba kwinkqubo zophendlo lwezifo imiba efanayo yemfuza. Ngokukodwa, ngokubhekiselele kwizinto ezifana lolu phando-galotipy.

Symptomatology entsifalita Rasmussen

Ekuqaleni, esi sifo ibonisa ukugula motor focal. Njengokuba isifo ukujoyina myoclonus zasekuhlaleni. Ekuhambeni kwexesha, kuhlasela enomfutho. Bona kunye aqaqambayo, ukulahlekelwa sezingqondweni bawe. Ngokufuthi, izigulane sihlaselwa ngexesha bubuthongo.

Phambili, esi sifo kubonakala kuphelelwa ngamandla kunye antsi buso ibakho nayiphi na ilungu lomzimba indlebe. Uphando lubonisa ukuhla kumsebenzi kummandla ebuchotsheni ochaphazelekayo.

ekuxilongweni

Iimpawu awasiwisayo abantu ukubandezeleka unyaka kunye syndrome of Rasmussen. Kobuchopho kunye umyalezo zokuzama ukuchonga kwangethuba kangangoko kunokwenzeka. Oku kukuvumela ukuba nethemba nempembelelo entle unyango immunosuppressive. Ngoko yokuqala lonke bathelela isifundo lwesifo, MRI kunye EEG lwenziwa.

Iindlela zonyango lwe kobuchopho Rasmussen kaThixo

Ngokuba kunjalo kude kukho iimbambano ngezinto ezibangela Rasmussen engqondweni, kobuchopho singanyangwa ngeendlela eziqhelekileyo. Ukuba efumanise kusekwangoko isifo amisele amayeza antiepileptic umlinganiswa. Ncoma ukutya eziyilelwe ukwandisa ukusetyenziswa okune kukutyeba, nokuncipha imali kukutya ukutya okuneekhabohayidrithe. Amaxesha amaninzi kukufumanisa kuluncedo ukusebenzisa plasmapheresis, corticosteroids, immunoglobulins.

Ngokufuthi, unyango sifo aze asebenzise iindlela olukhulu. Izigulane ubunzima ukugula kakhulu ukwenzakala ebuchotsheni ezintsonkothileyo, kuyimfuneko ukwenza nokufakelwa iiseli zemithambo-luvo. Ngoku kangangoko kunokwenzeka sizama ukuba baqhube craniotomy.

Ngamanye amaxesha izigulane wanikela ungenelelo ngotyando - Hemispherectomy. Emva kube lula ukuba Rasmussen engqondweni. Kobuchopho, Kakade, ishiya imizila zayo, paresis ngokukhawuleza okanye neengxaki intetho. Noko ke, ehlasela isigulane azixhaphakanga.

Ukunika up uqhaqho akufuneki, nakubeni oko akuthethi kukhokelela ukugqibezela impiliso. Ngapha koko, uphuhliso sifo aggravates yokushota luvo emizamweni yabo, apho kukho ukukhubazeka engqondweni kunye nokukhubazeka.

Kwiimeko amanxeba zokubonisana zobuchopho (zombini zifaka) ukuqikelela ngelishwa nezinzima. Amatyala yokufa phakathi kwezigulane kobuchopho Rasmussen nto ingaqhelekanga.