Zempilo, Emehlweni
Fuchs endothelial muscular. Yintoni muscular Fuchs '
Corneas imele i lwangaphandle ngaphambili eyenzelwe ukwenza ukhuseleko, ifayibha optic, kunye nokusebenza vlagoprodutsiruyuschuyu refracting. Le inwebu usengozini kukwenzakala ngaphezu kwezinye iindawo iliso enokukhokelela angakwazi yayo.
Yintoni muscular: uhlobo muscular
muscular kwenwebu yamehlo iquka uluhlu olubanzi izifo ekhokelela inkungu phambi zangaphandle inwebu iso. Ngokuxhomekeke kuyo inwebu le inwebu wambetha yi (abangama-ezintlanu), kukho iintlobo ezininzi sifo:
- ifomu muscular epithelial, kukungakwazi ukukhusela iiseli epithelial okanye inani labo labayo;
- inwebu muscular, apho bekuhleli kuyondelelaniswe engachanekanga iiprotheni kwenwebu;
- ifomu dystrophies stromal, Vuka ngenxa utshintsho stroma;
- endothelial ifomu muscular - oku Fuchs muscular.
Izinto ezibangela muscular
muscular imbangela siyifumana umonakalo izakhi ezithile. Khangela zolwaphulo baya kuphela emxinwa-analysis, emva kokuba apho kunokwenzeka khona ukuba bathethe malunga nendlela yokuqala okanye yesibini yaloo dystrophy.
muscular prayimari njengelifa. Esi sifo abambiseneyo. akhawunti Development for abantwana okanye lokufikisa, uya ezingahambi ukudumba. ubuntununtunu umzimba yehliswe kancinci, ngokufuthi ngqalelo sisigulane.
esibulala japan Secondary emehlweni yokwenzakala emva izifo utyando, ukudumba okanye sokuhlasela.
uhlobo Endothelial lwesifo
nesifo Endothelial ebizwa Fuchs 'muscular libhekisela, iintlobo eziphambili yemfuza kwesi sifo. Makhe sithethe ngayo poodrobno ngakumbi.
Yintoni muscular Fuchs '? Oku kulimaza umaleko engaphakathi inwebu, elenza umsebenzi kwimpompo, zokumpompa le ulwelo ngokulandelelana kwayo. fluid kwemfuneko le inwebu ikhokelela turbidity yayo. Phambili, Fuchs muscular kukhokelela ngodungadungo ngokuthe ngcembe leseli endothelial.
Kangangexesha elithile, ukunqongophala Iseli ithathwa umsebenzi lwesamente eseleyo. Izigulane kusekwangoko isifo-eqongeni, zezomzuzwana ilahleko yombono ngexesha kusasa. Oku kungenxa ukufuma ukungakwazi vaporatsii ukusuka kumphezulu inwebu ebusuku, nto leyo sokuzuza yayo. Neenkophe Vula ukuvumela ukufuma ukuba ngumphunga ngokwendalo, oko kukhokelele kuqheleke karhulumente waphawula emini. Ekubeni ngeke ukubuyiselwa iiseli endothelial, baza kufa, ngokuba umbono lifinyele. Xa ukwehla ngokunzulu okukhawulezileyo msebenzi inokumiselwa ukufakelwa kwenwebu.
Symptomatology endothelial muscular
obubonakala kwezonyango muscular Fuchs 'lungabonakaliswa ngeendlela ezahlukeneyo: ukusuka nazimpawu ukuya rezey kakhulu ukhukuliseko ebonakalayo.
Kumanqanaba okuqala khona:
- ukungaboni, nto leyo eya kuphucula emini;
- xa ujonge lo ilitha umthombo wokukhanya;
- ubukho koluvo umzimba angaphandle emehlweni.
ngezifo Progressive uneempawu ezifana:
- uphathwe kwaye bomvu;
- photophobia;
- uvakalelo ekukhanyeni;
- udumba inwebu engaphandle iso.
Edematous kwenwebu muscular: Fuchs muscular
Epithelial-endothelial muscular kunokuba eziziprayimari nezizisekondari. Secondary ukubonakala lwakhe ngenxa yokwenzakala okanye emva kotyando. Esi sifo senzeka xa iliso elinye. muscular Bullous, Fuchs imbangela ichazwa njenge ikhaya, zoshishino okanye umothuko yotyando. Kwaye ke umahluko ophambili ukusuka ukungondleki lokuqala edematous indawo elilinganiselweyo lubandakanywe nezenzo nokudumba, kuyo iiseli esempilweni ekwaziyo lokuthath'indawo sinesiphene. Ukuqalisa sifo esibonakala clouding okungephi kwiingcamba enzulu inwebu kunye ukudumba okuncinane. Ukuqhubela phambili le sifo kukhokelela kumlinganiselo nangakumbi iyalibala kunye inkungu, uburhabaxa kunye ukubonakala amaqamza amancinci kwi inwebu. Kukho photophobia ukwanda kunye neentlungu.
lokufunyaniswa kwesifo
Fuchs endothelial muscular isifo zamehlo. Ngexesha reception, ugqirha kuphela sihlolisise inwebu kunye isibane lisikwe, kodwa uqokelele imbali sifo. Ngaphandle pachymetry ultrasound obonisa ubukhulu kwenwebu kuncede ukuhlola iqondo ukudumba zingasetyenziswa.
microscopy Endothelial kuvumela ukubala inani leeseli endothelial square nawethu nganye.
unyango muscular
I lokuqala sifo zibandakanya unyango zemveli kunye ngamathontsi kunye namafutha eye ezikhuthaza nokuphelisa kolwelo ukusuka inwebu. Kodwa unyango elondoloza ukucola kuphela phantsi inkqubo ukutshatyalaliswa inwebu. IXesha ekuPhulukenwe nalo kungaba kwaqinisekiswa kuphela uqhaqho. ukususwa laser Xa inwebu epithelial okanye Zityeketyeke asetyenziswe ngayo isabelo izifo. Umonakalo ingxenye yaso nethala abohlukeneyo kwenwebu. Maxa wambi kuyimfuneko ukugqiba ukususwa inwebu engundoqo. Ingcaciso yale inwebu emva yokuntlokothiswa ngotyando ibuyiselwe, iimpawu ndimke. Kodwa ngamanye amaxesha muscular Fuchs 'Inokwenzeka kwakhona emva kweminyaka embalwa, nto leyo eya kukhokelela kwakhona yokuphatha-.
amanyathelo othintelo
Abaguli abafuna uncedo lonyango kwi zigaba zokuqala zesi sifo, ukunceda lula. Le oluntsonkothileyo amanyathelo othintelo kufuneka ibandakanye ukudla, ekubeni iiseli ngamandla le inwebu luxhomekeke ngqo ngoko isigulane odlayo. Ukutya kufuneka kube okunesondlo kunye okunezakha-mzimba kunye kwaqukwa kuyo imifuno kunye neziqhamo. Ngokwendalo kufuneka aphephe zonke ukwenzakala bafune unyango xa kuthe mizwa vumba emehlweni.
Ubude ubuthongo isigulane kunye ukuthambekela esi sifo kufuneka iiyure ezisibhozo, ngokuvumela kakuhle umzimba nokuphumla, yaye oku, nto iya kuthintela iingxaki kunye inwebu iso. Ekuchongeni muscular okunene ayifanele ukuba nesigqubuthelo lenses, nto leyo mandundu le meko.
Ngu muscular inwebu kunokukhokelela izinto njengelifa kunye nokwenzakala, umonakalo okanye sifo iziko umbono. unyango esifaneleke uncedo lwezonyango kunye nohlolo ngamaxesha lokunqanda kuya kusinceda ukuba sibe sibi kwaye kakhulu ngcono imeko yomzimba yesigulane.
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