Zempilo, Diseases and nemibandela
Isifo Butterfly: Iimpawu kunye Indlela Treatment
Epidermolysis bullosa, okanye ibhabhathane izifo - isifo obunqabileyo yingozi. Olu hlobo zofuzo dermatitis, nto leyo zibandakanya bekhubazekile kubume kwesikhumba. Ngelishwa, ukuza kuthi ga ngoku akukho unyango kakuhle onokugula okunjalo.
isifo Butterfly: ngoonobangela kunye iimpawu. Njengoko sele kukhankanyiwe, isifo elinjalo ilifa kwaye livela, njengoko umthetho, ngoko nangoko emva kokuzalwa. Kutheni na kwesi sifo ndinaso? Okokuqala kufuneka ukuba siqwalasele ubume ulusu ophilileyo.
Xa abantu, umaleko eliphezulu ulusu okanye esingaphandle, kujongwe ukuba ukukhusela ngokuchasene ifuthe kokusingqongileyo. Yena ngokuqhelekileyo idityaniswe ibhola nzulu - i dermis. Izigulane unesifo "ibhabhathane sifo" uqhagamshelwano phakathi sangaphandle kunye dermis ezingekhoyo okanye akukho yomelele, ukuba iphathe zonke kunokudala isikhumba kunye. Kungenxa yoko le nto isikhumba umntwana onjalo ubethwa yokwenzakala.
Epidermolysis bullosa kubonakala kwangoko emva kokuzalwa. Kubonakala phezu izilonda ulusu kunye nezilonda nkqu nempembelelo encinane lwangaphandle. Ukuba umntwana uza into, ngoko eluswini kufuneka kubonakala kwangoko. Kakade ke, isifo yebhabhathane ihamba ubuhlungu.
Njengoko esi sifo ikwachaphazela kwiinwebu amehlo, umlomo, kwingqula, ngenxa apho kuba kunzima ukondla umntwana. Xa inyathelo kamva inokubonakalisa mazinyo, umonakalo isifo esophageal kunye emathunjini.
Kakade, esi sifo ayikho butterfly obulalayo. Kodwa ke ukuhlala kule meko kunzima. Ukongeza, amanxeba abasisigxina, izilonda kakubi ephilisa kunye namadyungudyungu ke namasango entle fungal, iintsholongwane kunye nosulelo wentsholongwane egazini. Xa kungekho uphuhliso unonophelo nokudumba eyimfuneko eziqwalaselwa ukubonakala nakujoliso olutsha of necrosis.
Epidermolysis bullosa: unyango. Ngelishwa, isifo esinganyangekiyo namhlanje. Unyango eziphambili zenzelwe ukuba ukuthintela usuleleko kunye nokudumba nophuhliso.
Kwezinye iimeko, umntwana kufuneka unyango rhoqo glucocorticoids. unyango olunjalo inceda ukuthintela imbonakalo yabangxamayo kunye namadyungudyungu kakhulu eluswini, inwebu yangaphakathi, nezibilini. Ngamanye amaxesha nokunyanga kunye immunomodulators, ezinceda nezifo emzimbeni ekulweni.
Umntwana egulayo udinga ukunakekelwa rhoqo, nto leyo equka kweentsholongwane rhoqo amanxeba kunye zokubopha. Amanxeba iphathwa yomnquma ioli, iivithamini, izisombululo, namafutha enesiqulatho nemithi, infusions womfuno amayeza. kuluncedo kakhulu ulusu isigulana ibhafu kwezonyango kunye decoction oki amaxolo, ulandelelwano, chamomile okanye isisombululo ezibuthathaka potassium permanganate.
ingqalelo ekhethekileyo kufuneka inikwe ukutya. Kwinyanga yokuqala yobomi, webele-ibele kuyimfuneko. Kamva ukutya kufuneka fluid, ngaphandle ityuwa, iziqholo okanye naziphi iimveliso kukucaphukisa. Emva zokuxheshisela, umntwana kufuneka pula umlomo wakho olufudumeleyo, zifunxe ngamanzi - oku kuthintela ukuvela amagwebu, iyabhiqiza phezu iintsini.
Shoes nempahla kufuneka sithambile wenza kuphela evela amalaphu zendalo. Ukuba amathambo azinikezelwanga gqitha, umntwana kufuneka ukususa - oku kuya kunceda ukuthintela imbonakalo contractures.
Isifo idla sikhatshwe nophuhliso anaemia ibhabhathane, nto leyo eyingozi kakhulu ukuba umntwana egulayo. Kuyimfuneko ke ngoko ukuba esweni rhoqo isimo igazi, yaye ukuba kuyimfuneko - ukutofelwa plasma kunye albumin.
Ngamanye amaxesha isetyenziswa kunyango "Tocopherol acetate" - ichiza okuvuselela ukuveliswa imicu elastic collagen le dermis. Therapy ithatha indawo kwizigaba ezininzi, kwaye lubandakanya izifundo ezininzi ngokuphindaphindiweyo. Ngokuba ezinye izigulane, kuba le unyango Waba lusindiso.
Kuyo nayiphi na imeko, ibhabhathane izifo - ukugula kakhulu ukuba ufuna unyango rhoqo.
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